Gastrointestinal complications of the Ehlers-Danlos syndrome
نویسندگان
چکیده
منابع مشابه
Gastrointestinal complications of the Ehlers-Danlos syndrome.
The gastrointestinal abnormalities encountered in 125 patients with the Ehlers-Danlos syndrome have been described. Spontaneous perforation of the intestine and massive gastrointestinal haemorrhage are uncommon but potentially lethal complications of the Ehlers-Danlos syndrome. Less dangerous abnormalities, such ;as external hernia, hiatus hernia, eventration of the diaphragm, intestinal divert...
متن کاملLethal complications of the Ehlers-Danlos syndrome.
Death from arterial bleeding or gastrointestinal perforation has previously been reported in more than 15 patients with the Ehlers-Danlos syndrome. On a basis of 100 personally examined patients and a review of published accounts, these events seem particularly likely to occur in two distinct and recognizable forms (the gravis and the ecchymotic forms) of the syndrome.
متن کامل[Ehlers-Danlos syndrome].
We have described a patient with type 4 Ehlers-Danlos syndrome who died of a ruptured pulmonary artery. Of the six subtypes of Ehlers-Danlos syndrome, which can usually be clinically differentiated, only types 1 and 4 appear to be associated with a substantial risk of arterial rupture.
متن کاملSerious ophthalmological complications in the Ehlers-Danlos syndrome.
The main features of the Ehlers-Danlos syndrome (EDS) are cutaneous hyperextensibility, articular laxity, and fragility of the tissues. Systemic ramifications may lead to orthopaedic, cardiovascular, and gastrointestinal problems. Minor ophthalmological changes, including epicanthic folds, strabismus, and myopia are not infrequent, but serious ocular complications are rare. However, there have ...
متن کاملGastrointestinal surgery and related complications in patients with Ehlers-Danlos syndrome: a systematic review.
INTRODUCTION Ehlers-Danlos syndrome (EDS) is a rare inherited group of connective tissue diseases characterized by joint hypermobility, skin hyperextensibility and bruising tendency. Common features of patients with EDS include vascular and gastrointestinal perforations. The purpose of this systematic review is to address gastrointestinal diseases and the complications associated with surgical ...
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ژورنال
عنوان ژورنال: Gut
سال: 1969
ISSN: 0017-5749
DOI: 10.1136/gut.10.12.1004